Ventricular Tachicardia as a Form of Presentation of Isolated Noncompaction of Left Ventricular Myocardium

Author(s): M-José Gérez Callejas, José-Tomás Gómez Sáenz, Jaione González Aguilera, Rosario Zangróniz Uruñuela, Ángeles Blanco Mardones, Ana Ibáñez Castro and Yanett Orellana Fuentes

Isolated ventricular noncompaction left ventricular (LVNC) is a rare genetic disease characterized by left ventricular hypertrabeculation. Clinically manifested as systolic dysfunction, heart failure, ventricular arrhythmias, thromboembolic events and sudden death. It can occur alone or in combination with other congenital heart disease and / or neuromuscular disorders. It is diagnosed by echocardiography and magnetic resonance imaging and has a poor prognosis with amortality rate of 60-80%at 6 years, half of sudden death (SD). We present a case of LVNC which debuted as ventricular tachycardia.

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